Lhermitte-Duclos Disease (Dysplastic Cerebellar Gangliocytoma) in a Young Patient

Lhermitte Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar neoplasm. It usually presents with raised intracranial pressure along with cerebellar signs. We report a rare case of Lhermitte Duclos disease of a 20 years male who presented with signs & symptoms of raised intracranial tension. CT features were suggestive of Lhermitte-Duclos disease. Subtotal excision of the mass followed by histopathological evaluation confirmed the diagnosis. This case has been reported to emphasize clinical presentation and radiological features of this rare entity.